腸(chang)(chang)系(xi)膜(mo)上(shang)動(dong)脈(mo)壓迫(po)綜(zong)(zong)(zong)合(he)(he)癥(zheng)(zheng)(zheng)是指(zhi)十二(er)(er)(er)指(zhi)腸(chang)(chang)水平(ping)部(bu)受腸(chang)(chang)系(xi)膜(mo)上(shang)動(dong)脈(mo)壓迫(po)所致的急、慢性(xing)腸(chang)(chang)梗阻,亦稱(cheng)腸(chang)(chang)系(xi)膜(mo)上(shang)動(dong)脈(mo)綜(zong)(zong)(zong)合(he)(he)癥(zheng)(zheng)(zheng)、十二(er)(er)(er)指(zhi)腸(chang)(chang)血管壓迫(po)綜(zong)(zong)(zong)合(he)(he)癥(zheng)(zheng)(zheng)、良(liang)性(xing)十二(er)(er)(er)指(zhi)腸(chang)(chang)淤滯癥(zheng)(zheng)(zheng)或(huo)Wilkie綜(zong)(zong)(zong)合(he)(he)癥(zheng)(zheng)(zheng)。在骨科,應用石(shi)膏床及髖穗(sui)形石(shi)膏固定后,患者因過伸(shen)姿(zi)勢常會(hui)發生急性(xing)腸(chang)(chang)系(xi)膜(mo)上(shang)動(dong)脈(mo)壓迫(po)綜(zong)(zong)(zong)合(he)(he)癥(zheng)(zheng)(zheng),故又稱(cheng)為石(shi)膏綜(zong)(zong)(zong)合(he)(he)癥(zheng)(zheng)(zheng)(Cast綜(zong)(zong)(zong)合(he)(he)征)。
本(ben)病(bing)(bing)可(ke)發生(sheng)于任何年(nian)(nian)齡,瘦長(chang)體型的中青年(nian)(nian)多見(jian),根據發病(bing)(bing)情(qing)況可(ke)分為急性(xing)和慢(man)性(xing)兩(liang)類(lei)。慢(man)性(xing)患者癥(zheng)狀(zhuang)發作與體位(wei)(wei)有關,患者常可(ke)通(tong)過(guo)改(gai)變體位(wei)(wei)來減輕痛苦(ku),如側(ce)臥、俯臥、胸膝位(wei)(wei)、前傾坐(zuo)位(wei)(wei)或將雙(shuang)膝放在頜下等。反之,仰臥位(wei)(wei)可(ke)使癥(zheng)狀(zhuang)加重。急性(xing)腸(chang)系(xi)膜(mo)上動(dong)脈壓迫綜合征較少見(jian),病(bing)(bing)因多與創傷及醫源性(xing)因素有關,癥(zheng)狀(zhuang)與慢(man)性(xing)者相似,但癥(zheng)狀(zhuang)持續(xu)而嚴重,嘔吐頻繁而量大。
治(zhi)(zhi)(zhi)療(liao)(liao)方(fang)面有(you)保守治(zhi)(zhi)(zhi)療(liao)(liao)、手術治(zhi)(zhi)(zhi)療(liao)(liao)及介入治(zhi)(zhi)(zhi)療(liao)(liao)等。除了(le)因動脈瘤等需要立即手術或介入治(zhi)(zhi)(zhi)療(liao)(liao)的因素所致(zhi)的腸(chang)系膜上動脈壓(ya)迫(po)綜合癥外,急性發作期應首先采(cai)用保守治(zhi)(zhi)(zhi)療(liao)(liao),給予禁(jin)食、胃(wei)腸(chang)減壓(ya)、維持水(shui)、電解質和酸(suan)堿平衡及營養(yang)支持治(zhi)(zhi)(zhi)療(liao)(liao),必要時(shi)采(cai)用完全胃(wei)腸(chang)外營養(yang)。